Recurrent cutaneous angiosarcoma of the ear masquerading as atypical fibroxanthoma

AFX: atypical fibroxanthoma ERG: erythroblast transformation-specifice related gene INTRODUCTION Cutaneous angiosarcoma is a rare, malignant, vascular neoplasm of the skin commonly diagnosed in the head and neck regions. Involvement of the ear is rare. Although no definitive surgical guidelines exist, wide resection with possible adjuvant chemoradiation is generally accepted as the standard treatment for resectable lesions. We present the case of an elderly man with extensive angiosarcoma of the ear masquerading as atypical fibroxanthoma (AFX) necessitating total auriculectomy and combined radiation therapy. Our case also shows the utility of the erythroblast transformationspecificerelated gene (ERG) staining for difficultto-diagnose angiosarcomas.